Transmissible Spongiform Encephalopathies
ANIMAL TSEs
Host: mule deer, white-tailed deer, elk, moose
Experimentally transmitted to: cattle, sheep, squirrel monkey, ferret, mink, goat, Syrian golden hamster, Chinese hamster, Siberian hamster, Armenian hamster, transgenic mouse
Strains: undetermined (may be at least two strains per Raymond, et al. 2007)
Human pathogen: unknown (no confirmed cases)
Biosafety Level: 2
Bovine Spongiform Encephalopathy (BSE, Mad Cow Disease)
Host: cattle (and various zoo animals: cheetah, puma, lion, tiger, ocelot, zebu, American bison, ankole, kudu, eland, arabian oryx, scimitar horned oryx, nyala, and gemsbok)
Experimentally transmitted to: sheep, goat, mouse, cynomolgus macaque, pig, mink
Strains: BSE (typical), H-Type, L-Type (BASE)
Human pathogen: yes
Biosafety Level: 3
Host: sheep, goat, moufflon
Experimentally transmitted to: cattle, elk, capuchin, spider monkey, squirrel monkey, cynomolgus macaque, rhesus monkey, gerbil, hamster, mink, mouse, rat, vole
Strains: 22L, 139A, 79A, ME7, 22C, 301C, 22F, 87A, 22H, 79V, 301V, 22A, 87V, 111A, 34W, Nor98
Human pathogen: unknown (no confirmed cases)
Biosafety Level: 2
Transmissible Mink Encephalopathy (TME)
Host: mink
Experimentally transmitted to: cattle, squirrel monkey, rhesus monkey, stump-tailed macaque, ferret, goat, hamster, opossum, raccoon, sheep, skunk, sable, marten
Strains: HY, DY
Biosafety Level: 2
Feline Spongiform Encephalopathy (FSE)
Host: domestic cat
HUMAN TSEs
Host: human
Experimentally transmitted to: mink, ferret, squirrel monkey, chimpanzee, gibbon, capuchin, marmoset, spider monkey, woolly monkey, African green monkey, bonnet monkey, cynomolgus macaque, mangabey, rhesus monkey, pig-tailed macaque
Sporadic Creutzfeldt-Jakob Disease (CJD, sCJD)
Host: human
Experimentally transmitted to: guinea pig, cat, ferret, hamster, chimpanzee, capuchin, marmoset, spider monkey, squirrel monkey, woolly monkey, African green monkey, bushbaby, cynomolgus macaque, mangabey, patas, rhesus monkey, pig-tailed macaque, stump-tailed macaque, goat
Variant Creutzfeldt-Jakob Disease (vCJD, nvCJD)
Host: human
Gerstmann-Sträussler-Scheinker disease (GSS)
Host: human
Experimentally transmitted to: chimpanzee
Fatal Familial Insomnia
Host: human
Experimentally transmitted to: chimpanzee